Figure 2.12 A: Nevus sebaceus* B: Nevus sebaceus* C: Trichoepitheliomas* * Courtesy of Dr. Paul Getz
Presents as solitary yellow-orange slightly raised plaque typically on scalp or face; plaque typically thickens and becomes more verrucous or pebbly during childhood
Mutation in PTCH gene has been reported (deletion)
Benign tumors (trichoblastoma, syringocystadenoma papilliferum) and malignant tumors (BCC < 1% cases) can arise within lesion