Cowden Syndrome (Multiple Hamartoma Syndrome) (Figure 2.22C) | Figure 2.22
A: Angiofibromas in TS
(Courtesy of Dr. Michelle
B. Bain)
B: Koenen tumor in TS
(Courtesy of Dr. Paul Getz)
C: Cowden syndrome
(Reprint from Morgan MB,
Smoller BR, Somach SC.
Deadly Dermatologic Diseases.
New York, NY: Springer; 2007) |
- Trichilemmomas (smooth to verrucous small papules on face), “cobblestone” appearance of the mucosa including tongue (oral papillomas), acral keratotic papules
- ↑ Breast fibroadenoma, ↑ CA: breast, thyroid follicular; GI polyps
| | | | | | COWden – trichileMOOmas; other PTEN syndromes: Lhermitte–Duclos and
Bannayan–Zonana syndrome | | | | | |
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